--- a +++ b/processing/MACCROBAT/26629302.txt @@ -0,0 +1,15 @@ +A 13 year-old boy presented with a 1 month history of intermittent episodes of small volume epistaxis. +There was no significant past medical, surgical or family history. +Physical examination revealed a left palatal fleshy mass centered at left posterior molars. +A nasoendoscopic examination demonstrated a large swelling on the floor of left anterior nasal space, involving the left inferior meatus and abutting the inferior turbinate. +Computed Tomography (CT) of the paranasal sinuses showed a lobulated, expansile lytic lesion of left maxilla [Fig 1] with a lucent center and peripheral calcifications. +The lesion was associated with a large soft tissue component that demonstrated mild heterogeneous contrast enhancement. +The lesion was centered at the left maxillary alveolus, involving the left hard palate, inferior part of the anterior left maxillary wall and medial left maxillary wall. +The lesion also involved the roots of the left maxillary molars and pre-molars and was abutting the left orbital floor, with no gross orbital invasion. +The patient subsequently underwent 18-FDG PET-CT study. +The mass centered in left maxilla was hypermetabolic, with index SUVmax 9.7 [Fig 2]. +There was no FDG-avid metastatic disease. +A trans-oral incisional biopsy of the left palatal mass was performed and was suggestive of a preliminary diagnosis of mesenchymal chondrosarcoma, as evidenced by a biphasic pattern featuring sheets of small round cells with hemangiopericytoma-like vascular pattern and mature cartilaginous islands. +The patient underwent left subtotal maxillectomy via lateral rhinotomy and translabial approach. +The final histology was conclusive of a 5cm high-grade (Grade 3) mesenchymal chondrosarcoma. +One of the resection margins was positive for tumor involvement and the patient was planned for adjuvant chemotherapy.