--- a +++ b/processing/MACCROBAT/22665582.txt @@ -0,0 +1,22 @@ +A 5-year-old Caucasian male presented to the Children’s Emergency Department with epistaxis, bleeding from the dental extraction site and a widespread purpuric rash, secondary to acute idiopathic thrombocytopenia. +Two days prior to this, he developed a generalised chickenpox rash. +While in the department it was noted that his heart rate ranged between 50 and 60 beats per min, he was otherwise haemo-dynamically stable with a normal blood pressure and oxygen saturations in air. +He had a short systolic murmur grade 2/6 at the left sternal border. +He had no clinical evidence of myocarditis or heart failure. +He had extensive generalised petechiae and purpuric rash (figure 1) secondary to acute thrombocytopenia presumed to be due to varicella infection. +Apparently he was healthy prior to this admission. +There was no history of maternal lupus. +An ECG was performed which showed complete heart block (figure 2). +He was admitted to the high dependency unit for close overnight monitoring. +The presumed diagnosis was complete heart block secondary to varicella infection.1 2 The initial investigation showed normal electrolytes, calcium, phosphate, glucose and magnesium levels. +The full blood count showed a normal haemoglobin and white cell count. +But the platelet count was low that is, 13×109/l. +The platelet count normalised within 10 days without any intervention. +The antinuclear antibody titres and the autoimmune screen were negative. +Maternal autoimmune screen was negative. +The echocardiogram showed a structurally normal heart and follow-up 24 h tape showed persistence of complete heart block. +Following these investigations a diagnosis of congenital complete heart block was made. +On follow-up after 6 months his heart rate remains between 50 and 60 beats per min, but he remains asymptomatic without any intervention. +The need for a pacemaker is being considered on follow-up. +The incidental finding of complete heart block was congenital in aetiology with no association with varicella infection or acute thrombocytopenia. +This case highlights that asymptomatic late-presenting congenital complete heart block must be considered as a differential diagnosis in children presenting with asymptomatic bradycardia to the emergency department.